Fígado policístico - relato de caso / Polycystic liver - case report

Authors

  • Vanessa Frajblat Brazilian Journals Publicações de Periódicos, São José dos Pinhais, Paraná
  • Maria Eduarda Ragghiante Ferreira
  • Viviane Lozano Espasandin

DOI:

https://doi.org/10.34117/bjdv7n6-424

Keywords:

Polycystic liver, Polycystic liver disease.

Abstract

Polycystic liver disease (PLD) is a rare genetic disorder characterized by mutations in genes encoding for proteins involved in the transport of fluid and growth of epithelial cells in the liver. There are two distinct forms of PLD; in isolation and in association with polycystic kidney disease (PKD) (1). The severity of the disease in patients with PKD is highly variable, meanwhile  the presence of liver cysts is the most important clinical feature of polycystic liver disease (2,3). There are currently several options of treatment available, including drug terapy and surgical optopns (1,4).

 

 

References

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Published

2021-09-24

How to Cite

Frajblat, V., Ferreira, M. E. R., & Espasandin, V. L. (2021). Fígado policístico - relato de caso / Polycystic liver - case report. Brazilian Journal of Development, 7(9), 92530–92539. https://doi.org/10.34117/bjdv7n6-424

Issue

Section

Original Papers