Uncommon presentations of angiofibroma in sinonasal tract: a two-case report/ Apresentações incomuns de angiofibromas no trato nasossinusal: relato de dois casos

Luísa Corrêa Janaú, Regiane Matos Batista, Ana Larisse Godim Barbosa, Luigi Ferreira e Silva, Leonardo Mendes Acatauassu Nunes, Diego Gadelha Vaz

Abstract


Juvenile nasopharyngeal angiofibroma (JNA) are rare, histologically benign, but locally aggressive, vascular tumors of the nasopharynx that affects predominantly male adolescents, its origins from other sites is denominated extranasopharyngeal angiofibroma (ENPA), which is an even rarer entity afflicting more females and young adults, representing a diagnostic and therapeutic challenge to rhinologists. In this report we present 2 cases of similar clinical presentation, with unilateral nasal obstruction and previous episodes of nasal bleeding. One patient is a 14-year-old male with a soft-tissue mass occupying nasopharynx, middle meatus, and right nasal cavity. The second patient is a 12-year-old male with a soft-tissue lesion rising from right sphenoid sinus and obliterating right nasal cavity, obstructing ipsilateral maxillary sinus, ethmoidal cells, and frontal sinus. Both patients underwent complete endoscopic excision of the lesions, the first one recurred on sphenoid sinus and the second showed no recurrence after 2 years of post-operative follow-up. The unusual sites and presentations make these rare cases and thus worth of reporting.


Keywords


juvenile nasopharyngeal angiofibroma, JNA, extranasopharyngeal angiofibroma, ENPA, endoscopic surgery.

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References


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DOI: https://doi.org/10.34119/bjhrv3n6-101

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